It is important to understand the underlying causes and the complications of the disease. Acute chest syndrome is one of the leading causes of death associated with sickle cell disease. It is critical to understand how to care for these patients holistically. Pathophysiology Sickle cell disease is a genetic condition that causes a mutation in the hemoglobin molecule.
Sickle Cell Anemia Hesi Education
HESI Case Studies--Pediatrics-Sickle Cell Anemia (Mary) | reeg.info
A child who inherits the two copies of the sickle mutation will be diagnosed as having sickle cell anemia with hemoglobinSS, also designated as Hgb SS. One who inherits a copy of a sickle hemoglobin gene mutation from one parent and a normal hemoglobin gene from the other parent will have HgbAS, which renders the child a carrier of the sickle cell trait. Both parents who carry a normal hemoglobin gene and the sickle cell hemoglobin are usually healthy carriers heterozygotes of the sickle trait HgbAS ; they will have inherited this trait, and it is a condition that under normal circumstances will not make them sick. However, under certain conditions for instance, low oxygen tension at very high altitudes , having the sickle trait can lead to health problems such as hematuria blood in the urine , pain, splenic sequestration blood entrapment or pooling of blood in the spleen , and sudden death.
Critical Care Nursing: Sickle Cell Anemia
A year-old woman with a history of sickle cell disease SCD presents to the clinic for follow-up after a hospitalization for a vaso-occlusive pain crisis complicated by influenza A. She has a history of an acute ischemic stroke at age 5 years and has received monthly, simple red cell transfusions since the stroke. Her last transfusion was approximately four months prior.
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